Rickettsia rickettsii is a tick-borne illness and the etiologic agent of Rocky Mountain Spotted Fever (RMSF)
Epidemiology
Incidence – 3-5/1,000,000
Age – greatest incidence in children <10 years old
Transmission
Via Dermacentor and Amblyomma spp ticks in the U.S.
Humans are accidental hosts
95% of the cases occur April through September
Organism
Gram-negative coccobacilli which are obligate intracellular organisms
A characteristic feature of the Rickettsiae is that they multiply in an arthropod as part of their life cycle
With spotted fever, the invertebrate hosts are both reservoirs and vectors
Rickettsia are part of a family of organisms responsible for the following rickettsial diseases:
Spotted fever and typhus (vector: tick, louse, flea or gamasid mite)
Scrub typhus (vector: chigger)
Ehrlichiosis (vector: tick)
Neorickettsiasis
Q-Fever
Risk Factors
Dog exposure to ticks
Residence in a wooded area
Residence in Central and Mid-Atlantic States
Male gender
Clinical Presentation
The incubation period between tick bite and onset of symptoms is 2-6 days
Rocky Mountain Spotted Fever is difficult to differentiate from viral illness
Non specific signs and symptoms
Fever, headache and rash are the classic triad
Rash typically appears on the second or third day of illness
Rash begins as macules on the wrists, palms, ankles and soles of feet, then petechiae form
Rash finally spreads to the trunk
Rash is a hallmark of infection, but it usually follows systemic symptoms; its absence should not rule out a possible rickettsial etiology
Onset of disease is sudden in about half of the cases
Other symptoms include malaise, myalgias, vomiting and photophobia
Mild pulmonary involvement, manifested by cough and infiltrates, is found in about one-third of patients with Rocky Mountain Spotted Fever
Serious central nervous system impairment seen in 25% of patients
Mortality is dependent on cardiac and central nervous system involvement or delay in treatment
Diagnosis
Diagnosis is made based upon clinical grounds, symptoms and/or serology and history of tick exposure
The best evidence for infection is a significant change on 2 appropriately timed specimens where both tests are done in the same laboratory at the same time
Appearance of an IgM antibody response normally occurs 7-14 days after the onset of disease
Differential Diagnosis
Lyme disease
Human monotropic ehrlichiosis
Human granulocytic anaplasmosis
Parvovirus B19
Epstein-Barr virus
Disseminated gonococcus
Leptospirosis
Secondary syphilis
Kawasaki disease
Mycoplasma pneumoniae
Treatment
Initiation of early antibiotic therapy is necessary to reduce mortality
Determine if infection due to Rickettsia rickettsii (Rocky Mountain Spotted Fever)
Acute and convalescent titers may be necessary
Low-positive results suggest past exposure or infection, while high-positive results may indicate recent or past infection, but are inconclusive for diagnosis
Initial testing may not be helpful; determine treatment from clinical and other laboratory assessments
Method: Direct Agglutination/Enzyme-Linked Immunosorbent Assay/Immunofluorescence Assay
Use to confirm presence of disease; not recommended for initial testing
Panel includes IgM Rickettsia rickettsii antibody by ELISA testing; as well as testing for antibodies to Brucella, Rickettsia typhi, Salmonella O and H
Initial testing may not be helpful; determine treatment from clinical and other laboratory assessments
Additional Tests Available
Click on number for test-specific information in the ARUP Laboratory Test Directory
These tests are for antibodies to Rickettsia rickettsii. Any antibody reactivity to Rickettsia rickettsii should also be considered group reactive for the Spotted Fever group (Rickettsia conorii, Rickettsia honei, Rickettsia akari, Rickettsia japonica, Rickettsia australis, and Rickettsia sibirica).
While the presence of IgM antibodies suggests recent infection, low levels of IgM antibodies may occasionally persist for more than 12 months post-infection.
If antibody test results are equivocal, consider retesting in 10-14 days.
Culture testing
Available only in research laboratories.
Guidelines
Chapman AS, Bakken JS, Folk SM, Paddock CD, Bloch KC, Krusell A, Sexton DJ, Buckingham SC, Marshall GS, Storch GA, Dasch GA, McQuiston JH, Swerdlow DL, Dumler SJ, Nicholson WL, Walker DH, Eremeeva ME, Ohl CA.Diagnosis and management of tickborne rickettsial diseases: Rocky Mountain spotted fever, ehrlichioses, and anaplasmosis--United States: a practical guide for physicians and other health-care and public health professionals.MMWR Recomm Rep. 2006;55(RR-4):1-27. (Link to PubMed)
General References
Buckingham SC.Rocky Mountain spotted fever: a review for the pediatrician.Pediatr Ann. 2002;31(3):163-168. (Link to PubMed)
Comer JA, Paddock CD, Childs JE.Urban zoonoses caused by Bartonella, Coxiella, Ehrlichia, and Rickettsia species.Vector Borne Zoonotic Dis. 2001;1(2):91-118. (Link to PubMed)
Consequences of delayed diagnosis of Rocky Mountain spotted fever in children--West Virginia, Michigan, Tennessee, and Oklahoma, May-July 2000.MMWR Morb Mortal Wkly Rep. 2000;49(39):885-888. (Link to PubMed)
Paddock CD, Zaki SR, Koss T, Singleton J Jr, Sumner JW, Comer JA, Eremeeva ME, Dasch GA, Cherry B, Childs JE.Rickettsialpox in New York City: a persistent urban zoonosis.Ann N Y Acad Sci. 2003;990:36-44. (Link to PubMed)
Sexton DJ, Kaye KS.Rocky mountain spotted fever.Med Clin North Am. 2002;86(2):351-viii. (Link to PubMed)
Reviewed by
Litwin, Christine, M.D. Medical Director, Immunology at ARUP Laboratories; Professor, Clinical Pathology, University of Utah
Comprehensive Review: September 2007
Last Update: September 2007