Echinococcosis infection is caused in humans by the larval stage of cestodes belonging to the genus Echinococcus.
Epidemiology
Prevalence – endemic in Eurasia, South America and Africa
In North America – most cases occur in immigrants from endemic countries
Transmission – fecal-oral route
Organism
3 species – E. granulosus, E. multilocularis and E. vogeli
The minute tapeworm, E. granulosus, develops in the intestine of dogs and other Canidae; prevalent where livestock are raised in association with dogs
Its larval stage, the hydatid cyst, may be found in many mammals (cattle, sheep, hogs, man) when the eggs are ingested
The adult worm is present only in dogs
Cysts develop in intermediate hosts (human, sheep, cattle, goats)
Hydatid cysts may form in any organ or tissue in humans; most commonly seen in the liver, lung and central nervous system
In humans, the embryo develops slowly into hydatid cysts, reaching a diameter of 1 cm in 5 months or so; at the end of 10 or more years, they may contain liters of fluid
The cysts vary considerably in size, depending on their age and location
Cysts may or may not be able to expand freely depending on the location in the body
In some cases, even a modest growth will result in serious impairment to the function of vital structures and even death
Clinical Presentation
Hepatic disease is the most common presentation and may present as abdominal pain or a palpable right upper quadrant mass (about 2/3 of patients)
Lungs are the second most common site of involvement of cysts
Rupture of cysts leads to multifocal dissemination
Diagnosis
Indications for testing – clinical evidence by MRI/US may provide evidence for testing
Laboratory testing
Serum antibody screening
Positive antibody response occurs in 90% of liver cysts, but only in 50% of lung cysts
Most sensitive testing by ELISA and IFA methods
Diagnosis prior to any surgery is recommended; aspiration of cysts is discouraged since this may result in fluid leakage and dissemination
Treatment
Involves percutaneous aspiration, infusion of scolecoidal agents with reaspiration or surgery
Tests generally appear in the order most useful for common clinical situations
Click on number for test-specific information in the ARUP Laboratory Test Directory
Test Name and Number
Recommended Use
Limitations
Follow Up
Echinococcus Antibody, IgG, Serum by ELISA 0050250
Method: Enzyme-Linked Immunosorbent Assay
Confirm suspicion of Echinococcus parasite invasion in humans
Patients with collagen vascular diseases, hepatic cirrhosis, schistosomiasis and other parasitic infections can produce false-positive results
There is a strong cross-reaction between echinococcosis and cysticercosis positive sera
Additional Information
Antibody testing
If antibody test results are equivocal, consider retesting in 10-14 days
Seroconversion between acute and convalescent sera is considered strong evidence of recent infection
The best evidence for infection is a significant change on 2 appropriately timed specimens where both tests are done in the same laboratory at the same time
General References
Carmena D, Benito A, Eraso E.The immunodiagnosis of Echinococcus multilocularis infection.Clin Microbiol Infect. 2007;13(5):460-475. (Link to PubMed)
Eckert J, Deplazes P.Biological, epidemiological, and clinical aspects of echinococcosis, a zoonosis of increasing concern.Clin Microbiol Rev. 2004;17(1):107-135. (Link to PubMed)
Filippou D, Tselepis D, Filippou G, Papadopoulos V.Advances in liver echinococcosis: diagnosis and treatment.Clin Gastroenterol Hepatol. 2007;5(2):152-159. (Link to PubMed)
Garcia HH, Moro PL, Schantz PM.Zoonotic helminth infections of humans: echinococcosis, cysticercosis and fascioliasis.Curr Opin Infect Dis. 2007;20(5):489-494. (Link to PubMed)
Ito A, Nakao M, Sako Y.Echinococcosis: serological detection of patients and molecular identification of parasites.Future Microbiol. 2007;2:439-449. (Link to PubMed)
Lorenzo C, Ferreira HB, Monteiro KM, Rosenzvit M, Kamenetzky L, Garcia HH, Vasquez Y, Naquira C, Sanchez E, Lorca M, Contreras M, Last JA, Gonzalez-Sapienza GG.Comparative analysis of the diagnostic performance of six major Echinococcus granulosus antigens assessed in a double-blind, randomized multicenter study.J Clin Microbiol. 2005;43(6):2764-2770. (Link to PubMed)
Siracusano A, Bruschi F.Cystic echinococcosis: progress and limits in epidemiology and immunodiagnosis.Parassitologia. 2006;48(1-2):65-66. (Link to PubMed)
Zhang W, McManus DP.Recent advances in the immunology and diagnosis of echinococcosis.FEMS Immunol Med Microbiol. 2006;47(1):24-41. (Link to PubMed)
Reviewed by
Litwin, Christine, M.D. Medical Director, Immunology at ARUP Laboratories; Professor, Clinical Pathology, University of Utah
Comprehensive Review: July 2008
Last Update: July 2008