Neuroblastoma is a common childhood neoplasm and is the most common extracranial solid tumor in children
Epidemiology
Risk Factors
Pathophysiology
Clinical Presentation
Diagnosis
Disease Monitoring
| Risk Group Classification | |||||
| Risk Group | INSS | Age | N-myc | DNA index | Shimada histopathology |
| Low | 1 2A, 2B 2A, 2B 2A, 2B 4S |
Any <1 ≥1 ≥1 <1 |
Any Any Nonamplified Amplified Nonamplified |
Any Any Any Any >1.0 |
Any Any Any Favorable Favorable |
| Intermediate | 3 3 4 4S 4S |
<1 ≥1 <1 <1 <1 |
Nonamplified Nonamplified Nonamplified Nonamplified Nonamplified |
Any Any Any 1.0 Any |
Any Favorable Any Favorable Unfavorable |
| High | 2A, 2B 3 3 3 4 4 4S |
≥1 <1 ≥1 ≥1 <1 ≥1 <1 |
Amplified Amplified Nonamplified Amplified Amplified Any Amplified |
Any Any Any Any Any Any Any |
Unfavorable Any Unfavorable Any Any Any Any |
| (Adapted with permission from Weinstein, et al., 2003, 282) | |||||
Prognosis